Frantz Tumor - Pseudopapillary Cystic Neoplasm of the Pancreas in Children: Report of Two Patients

Abstract

Pseudopapillary cystic neoplasm of the pancreas (Frantz tumor) is rare slow growing tumor with low malignant potential usually affecting young women. PCN have good prognosis in case of radical removal. Tumor was described for the first time by Frantz in 1959. A retrospective clinical analyses was made of two patients with PCN admitted in our hospital in the last 10 years. A 16 year old girl admitted in our hospital with intermittent abdominal pain lasting for 3 years. Abdominal ultrasound and CT-scan showed the presence of the tumor in a head of pancreas. Excision was performed. A 13 year boy came to routine US because frequent urological infection. Abdominal US and after CT are showed the presence of the tumor in a neck of pancreas. Excision was performed. In both of patients metastases were not noticed. The follow up period was 9 years in female patient and 2 years in male patient, Surgical resection of PCN affords an excellent prognosis without other ways of treatments.